A surgical management of melanotic prognoma tumor of Infancy – A case report

Shilpa Hazare; Isha Hazarey; Jitendra Hazarey; Pritish Bhansali; Vishal Mahant; Rashiqua Sadiya

doi:10.18502/bccr.v14i3.14355

Shilpa Hazare Dept. of Pediatrics & Neonatology, Getwell Hospital, Nagpur, India
Isha Hazarey Jawaharlal Nehru Medical College, Sawangi, Wardha, India
Jitendra Hazarey Getwell Hospital, Nagpur, India
Pritish Bhansali Getwell Hospital, Nagpur, India
Vishal Mahant Getwell Hospital, Nagpur, India
Rashiqua Sadiya Getwell Hospital, Nagpur, India

DOI: https://doi.org/10.18502/bccr.v14i3.14355

Keywords: case report, Lump in the maxilla, maxilla tumor, marginal mandibulectomy, melanotic neuroectodermal tumor of infancy.

Abstract

Melanotic neuroectodermal tumors (MNTI) also known as retinal anlage tumor and melanotic progonoma is highly aggressive lesion found in children within 6 months of age. It is a relatively rare pathology and is also rare to metastasise. MNTI can be seen in various locations within the oral cavity, the most common being maxillary jaw. Presently advent technology of has enabled us to utilise various different modalities ranging from radical excision, incomplete resection to chemotherapy. Chemotherapy is preferred in cases of contraindication of surgical approaches. The results regarding each approach can be mixed, successful tumour regression or complete failure. The present article focuses on successful subtotal excision of MNTI in a one year old infant.