Anaesthetic Management in a Child with Cutis Laxa for Bilateral Ureteric Reimplantation

Haripriya Ramachandran; Dammaningala Venkataramaiah Bhagya

doi:10.18502/aacc.v7i3.6907

Haripriya Ramachandran Department of Paediatric Anaesthesia, Indira Gandhi Institute of Child Health, Rajiv Gandhi University of Health Sciences, Bengaluru, India..
Dammaningala Venkataramaiah Bhagya Department of Paediatric Anaesthesia, Indira Gandhi Institute of Child Health, Rajiv Gandhi University of Health Sciences, Bengaluru, India.

DOI: https://doi.org/10.18502/aacc.v7i3.6907

Keywords: Paediatric anaesthesia; Cutis laxa; Difficult airway

Abstract

Cutis laxa is a rare congenital multisystem connective tissue disorder. Patients with cutis laxa can present with distinctive facial features, pulmonary emphysema and right-sided heart failure. Anaesthetic management is important because of difficult airway and respiratory/cardiac abnormalities. We have reported the preoperative evaluation and anaesthetic management of a child with Cutis laxa with right cleft lip and palate.