Airway Management in Pediatric MPS: A Case Report

Hasanali  Ahmadi; Farnaz Shahabi  Shojaei; Ehsan  Moradi; Nastaran Sadat  Mahdavi

doi:10.18502/aacc.v12i4.21809

Hasanali Ahmadi Department of Anesthesiology, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Farnaz Shahabi Shojaei Department of Anesthesiology, Mofid Children's Hospital, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Ehsan Moradi Department of Neurosurgery, Mofid Children's Hospital, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Nastaran Sadat Mahdavi Department of Anesthesiology, Mofid Children's Hospital, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, Iran.

DOI: https://doi.org/10.18502/aacc.v12i4.21809

Keywords: Mucopolysaccharidoses; Airway management; Anesthesiology; Case Report

Abstract

Mucopolysaccharidoses (MPS) refer to a group of disorders classified as congenital metabolic defects, characterized by airway management challenges because of facial deformities, macroglossia, short neck, hypertrophic tonsils and adenoids, kyphoscoliosis, an immobile jaw, narrowed nasal passages, and atlantoaxial instability. In this report, we present a case of successful management of a difficult airway in a pediatric patient with MPS.