Anaesthetic Management of Pediatric Patient with Osteogenesis Imperfecta Posted for Radius Ulna Nailing: A Case Report

Jyoti Deshpande; Shreya Rajendra Rawekar

doi:10.18502/aacc.v9i4.13532

Jyoti Deshpande Department of Anesthesiology, SMCW, Symbiosis International University, Pune, India.
Shreya Rajendra Rawekar Department of Anesthesiology, Smt.Kashibai Navale Medical College and General Hospital, Pune, Maharashtra, India.

DOI: https://doi.org/10.18502/aacc.v9i4.13532

Keywords: Osteogenesis Imperfecta; Total intravenous anaesthesia; Ultrasonography; Supraclavicular brachial plexus block

Abstract

Osteogenesis Imperfecta is a collagen disorder of autosomal dominant type caused by mutation of type COLIA-1 and COLIA-2 genes. Orthopaedic surgery in paediatric patient patients of OI is challenging mainly due to difficult airway and risk of malignant hyperthermia. Here we report, a paediatric case of OI with similar family history posted for radius ulna nailing which was managed with total intravenous anaesthesia and supraclavicular brachial plexus block.