Anaesthetic Management of Ebstein Anomaly in a Patient with Cleft PalateAnaesthetic Management of Ebstein Anomaly in a Patient with Cleft Palate

Sumaila Naaz; Anjum Saiyed; Reema Meena; Arun Garg

doi:10.18502/aacc.v9i3.13125

Sumaila Naaz Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India.
Anjum Saiyed Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India.
Reema Meena Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India.
Arun Garg Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India.

DOI: https://doi.org/10.18502/aacc.v9i3.13125

Keywords: Ebstein anomaly; Cleft palate; Ectrodactyly; Tachyarrythmias; Mitral Stenosis

Abstract

Ebstein anomaly is a challenge to the anaesthetist in terms of large right atrium, atrialised right ventricle and various valve abnormalities associated with it like Tricuspid Regurgitation(TR), Mitral Stenosis(MS), Mitral Regurgitation(MR).

In this case study, we report a 14-year-old female child presented with ebstein anomaly and cleft palate in our institution, SMS medical college & hospitals, Jaipur, Rajasthan. Cone’s operation was planned but due to multiple fenestrations in tricuspid leaflet only tricuspid and mitral valves were replaced. Patient was extubated next day with uneventful recovery.